| Local |
BNF | Section |
| Agalsidase | Agalsidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Fabry's Disease |
| Agalsidase | Agalsidase Beta | Nutrition And Metabolic Disorders, Metabolic Disorders, Fabry's Disease |
| Alglucosidase | Alglucosidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Pompe Disease |
| Asfotase | Asfotase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Hypophosphatasia |
| Avalglucosidase | Avalglucosidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Pompe Disease |
| Cipaglucosidase | Cipaglucosidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Pompe Disease |
| Elosulfase | Elosulfase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Mucopolysaccharidosis |
| Galsulfase | Galsulfase | Nutrition And Metabolic Disorders, Metabolic Disorders, Mucopolysaccharidosis |
| Hyaluronidase | Hyaluronidase | Musculoskeletal System, Soft Tissue And Joint Disorders, Soft Tissue Disorders |
| Idursulfase | Idursulfase | Nutrition And Metabolic Disorders, Metabolic Disorders, Mucopolysaccharidosis |
| Imiglucerase | Imiglucerase | Nutrition And Metabolic Disorders, Metabolic Disorders, Gaucher's Disease |
| Laronidase | Laronidase | Nutrition And Metabolic Disorders, Metabolic Disorders, Mucopolysaccharidosis |
| Ocriplasmin | Ocriplasmin [Specialist Drug] | Eye, Retinal Disorders, Vitreomacular Traction |
| Olipudase | Olipudase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Niemann-Pick Disease |
| Pancreatin | Pancreatin | Gastro-Intestinal System, Exocrine Pancreatic Insufficiency |
| Pegunigalsidase | Pegunigalsidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Fabry's Disease |
| Pegzilarginase | Pegzilarginase | Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders |
| Sebelipase | Sebelipase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Lysosomal Acid Lipase Deficiency |
| Velaglucerase | Velaglucerase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Gaucher's Disease |
| Velmanase | Velmanase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Alpha-Mannosidosis |
| Vestronidase | Vestronidase Alfa | Nutrition And Metabolic Disorders, Metabolic Disorders, Mucopolysaccharidosis |