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Bedfordshire and Luton Joint Formulary
Bedfordshire Hospitals NHS Foundation Trust
Bedfordshire, Luton and Milton Keynes ICB
Formulary Chapter: 9 - Nutrition and blood 
Notes:

Any drug not listed on the Formulary should be considered Non-Formulary - Not recommended for prescribing

09.08.01 Drugs used in metabolic disorders
09.08.01 Wilsons disease
09.08.01 Carnitine deficiency
09.08.01 Fabry's disease
09.08.01 Gaucher's disease
09.08.01 Mucopolysaccharidosis I
09.08.01 Pompe disease
09.08.01 Nephropathic cystinosis
09.08.01 Urea cycle disorders

Carglumic Acid 200mg (Carbaglu®)
(Dispersible tablets)

RED
Restricted Drug Restricted

For paediatric patients.

Kept in the L&D pharmacy EDC for use before patient transfer to a specialist hospital.

L-Arginine 5g /10mL
(Injection)

RED
Restricted Drug Restricted

For paediatric patients.

Kept in the L&D Pharmacy EDC for use prior to patient transfer to specialist hospital.

Sodium Benzoate 2g in 10mL
(Injection)

RED
Restricted Drug Restricted

For paediatric patients.

Kept in the L&D Pharmacy EDC for use prior to patient transfer to specialist hospital.

Sodium phenylbutyrate 1g in 5mL
(Injection)

RED
Restricted Drug Restricted

unlicensed unlicensed

For paediatric patients.

Kept in the L&D Pharmacy EDC for use prior to patient transfer to specialist hospital.

Non formulary items

Sodium Phenybutyrate (Ammonaps®)

 
Non Formulary
Classifications
May be initiated in any care setting
Specialist to advise therapy and provide first 28 days supply, continuation in Primary Care
Specialist to initiate and stabilise medicine prior to continuation in Primary Care
To be prescribed as per Shared Care Guidance. If no SCG in place status reverts to red.
Red medicines are designated as specialist only medicines which should only be prescribed by a specialist, usually within secondary care (either due to the requirement for specialist knowledge, long-term monitoring requirements, or restrictions that mean medicine supplies are only available to hospitals).
A decision has been made either locally and/or nationally not to routinely commission this preparation. Do not prescribe.
To be purchased over the counter. May be prescribed for chronic, long term conditions or on admission to hospital if essential.