Bedfordshire and Luton Joint Formulary
Bedfordshire Hospitals NHS Foundation Trust
Bedfordshire, Luton and Milton Keynes ICB
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Urea Cycle Disorders
Open monograph to display formulary status.
Formulary items found
Status
Description
Section
RED
Carglumic Acid 200mg Carbaglu
®
(Dispersible tablets)
Nutrition and blood, Urea cycle disorders, 09.08.01
RED
L-Arginine 5g /10mL
(Injection)
Nutrition and blood, Urea cycle disorders, 09.08.01
RED
Sodium Benzoate 2g in 10mL
(Injection)
Nutrition and blood, Urea cycle disorders, 09.08.01
RED
Sodium phenylbutyrate 1g in 5mL
(Injection)
Nutrition and blood, Urea cycle disorders, 09.08.01
Non Formulary items found
Status
Description
Section
Sodium Phenybutyrate Ammonaps
®
Nutrition and blood, Urea cycle disorders, 09.08.01
Searchiing the National BNF we found these items - Click button under Local to search local formulary or BNF to view on online BNF.
Local
BNF
Section
Carglumic
Carglumic Acid
Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders
Glycerol
Glycerol Phenylbutyrate
Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders, Drugs For Metabolic Disorders Ammonia Lowering Drugs
Pegzilarginase
Pegzilarginase
Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders
SODIUM
Sodium Benzoate
Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders
SODIUM
Sodium Phenylbutyrate
Nutrition And Metabolic Disorders, Metabolic Disorders, Urea Cycle Disorders, Drugs For Metabolic Disorders Ammonia Lowering Drugs