Bedfordshire and Luton Joint Formulary
Bedfordshire Hospitals NHS Foundation Trust
Bedfordshire, Luton and Milton Keynes ICB
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Cystic Fibrosis
Open monograph to display formulary status.
Formulary items found
Status
Description
Section
Amber SPA
Alpha Tocopheryl Acetate 500mg /5mL
(Suspension)
Nutrition and blood, Vitamin E, 09.06.05
GREEN
Carbomer 0.2%
Eye, Tear deficiency, ocular lubricants, and astringents, 11.08.01
Colistimethate Sodium 1 & 2 million units Colomycin
®
(Injection which can be nebulised)
Infections, Polymyxins, 05.01.07
RED
Dornase Alfa 2.5mg (2500 units) / 2.5mL Pulmozyme
®
(Nebuliser Solution)
Respiratory system, Dornase alfa, 03.07
RED
Tobramycin 300mg/4mL
(Nebuliser Solution)
Infections, Aminoglycosides, 05.01.04
RED
Tobramycin inhaler 28mg TOBI Podhaler
®
(Dry powder for inhalation)
Infections, Aminoglycosides, 05.01.04
Amber SPA
Vitamin and Mineral Supplement DEKAs
®
Plus
(Softgel capsules , chewable tablets , paediatric liquid )
A2 - Borderline substances, Vitamin and Mineral supplements, A2.04.02
Amber SPA
Vitamins ADEK capsules Paravit CF
®
(For Cystic Fibrosis)
A2 - Borderline substances, Vitamin and Mineral supplements, A2.04.02
Searchiing the National BNF we found these items - Click button under Local to search local formulary or BNF to view on online BNF.
Local
BNF
Section
Deutivacaftor
Deutivacaftor With Tezacaftor And Vanzacaftor
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Dornase
Dornase Alfa
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Ivacaftor
Ivacaftor
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Ivacaftor
Ivacaftor With Tezacaftor And Elexacaftor
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Lumacaftor
Lumacaftor With Ivacaftor
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Mannitol
Mannitol
Respiratory System, Diuretics, Osmotic Diuretics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Mannitol
Mannitol
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Tezacaftor
Tezacaftor With Ivacaftor
Respiratory System, Mucolytics
Conditions Affecting Sputum Viscosity, Cystic Fibrosis
Links found
JPC Bulletin: Use of Nebulised Tobramycin and Nebulised Colistimethate sodium as Antibiotic Prophylaxis to prevent exacerbations of Non- Cystic Fibrosis Bronchiectasis in Adult Patients
NICE NG78: Cystic fibrosis: diagnosis and management. October 2017
NICE TA1085: Vanzacaftor-tezacaftor-deutivacaftor for treating cystic fibrosis with 1 or more F508del mutations in the CFTR gene in people 6 years and over
NICE TA266 Cystic fibrosis - mannitol dry powder for inhalation (TA266)
NICE TA276: Cystic fibrosis (pseudomonas lung infection) - colistimethate sodium and tobramycin
NICE TA988 Evidence-based recommendations on ivacaftor–tezacaftor–elexacaftor (Kaftrio) plus ivacaftor (Kalydeco), tezacaftor–ivacaftor (Symkevi) plus ivacaftor, and lumacaftor–ivacaftor (Orkambi) for treating cystic fibrosis.